Listy klinické logopedie 2020, 4(2):51-55 | DOI: 10.36833/lkl.2020.0441277

Inner ear malformation

MUDr. Dagmar Hošnová, Ph.D.1, MUDr. Milan Urík, Ph.D.1
1 KDORL FN Brno a LFMU, FN Brno, Jihlavská 20, 625 00 Brno urik.milan@fnbrno.cz

Inner ear malformation comprises a broad group of disorders, the main symptom of which is hearing loss. The disorder occurs during the embryonic development of the auditory system. Only about 20 % of malformations can be diagnosed radiologically. Hearing impairment is sensorineural and can be of a mild degree, e.g. in the case of an enlarged vestibular aqueduct. However, more often, severe hearing loss is found. Hearing correction depends on the severity of the child's hearing impairment. Cochlear implantation in children with congenital profound hearing loss is optimal at the age of 12 to 24 months.

Keywords: inner ear, cochlea, hearing loss, cochlear implant

Received: October 5, 2020; Revised: November 17, 2020; Accepted: November 21, 2020; Published: December 14, 2020  Show citation

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Hošnová D, Urík M. Inner ear malformation. Listy klinické logopedie. 2020;4(2):51-55. doi: 10.36833/lkl.2020.044.
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